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R6dw@$!dk!z00 fB` % 6_V6Dg.X=kEE'HF} endstream endobj startxref 116 %%EOF Evolución a largo plazo de pacientes con miocardiopatía hipertrófica - Archivo PPCT

Evolución a largo plazo de pacientes con miocardiopatía hipertrófica;
Long-term Outcome of Patients with Hypertrophic Cardiomyopathy

Creators:Costabel, Juan Pablo, Ametrano, María C., Vrancic, Mariano, Cura, Fernando, Talavera, María L., Acosta, Adriana, Díez, Mirta, Sciancalepore, Agustina, Kuschnir, Paola, Avegliano, Gustavo
2016-06-28

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Descripción

Introducción: La miocardiopatía hipertrófica (MCH) es una enfermedad compleja, que ha sido asociada durante años a altas tasas de morbimortalidad. Sin embargo, mucha de la información que tenemos en relación a su evolución proviene de centros en donde se incluyeron pacientes seleccionados, principalmente de alto riesgo. El propósito del siguiente trabajo es evaluar los eventos en el seguimiento de pacientes con MCH en nuestro medio. Métodos: Se evaluó una cohorte retrospectiva de pacientes con diagnóstico de MCH. Se evaluó la evolución de la clase funcional, junto con la ocurrencia de eventos clínicos. Se recabaron datos del ecocardiograma y de la resonancia magnética cardíaca. Resultados: Se incluyeron un total de 259 pacientes, con una mediana de seguimiento de 3,5 años (2-10). La edad promedio fue de 56 ± 16,8 años y un 33 % tenían formas obstructivas. El 67 % de los pacientes estaban asintomáticos al inicio del seguimiento. En la evolución, la mortalidad global fue del 1,6 %, con un 1,1 % de muerte súbita y  un 6,6 % de los pacientes presentó fibrilación auricular. La tasa de internación por insuficiencia cardíaca resultó del 5,8 % y el 14,3 % de los pacientes empeoró su clase funcional. Se realizaron 22 procedimientos de ablación septal y 15 miectomías que mejoraron significativamente la sintomatología. Conclusión: este trabajo muestra que en el seguimiento de nuestros pacientes con MCH la tasa de morbimortalidad es baja, siendo el principal evento adverso el empeoramiento de la clase funcional, seguido por el desarrollo de FA y la insuficiencia cardíaca, con una baja tasa de muerte súbita.

Background: Hypertrophic cardiomyopathy is a complex disease that for years has been associated with high rates of morbidity and mortality. However, most of the available information on its outcome is based on data generated from centers including selected,mainly high risk patients.Objective: The purpose of this study was to evaluate the rate of events at follow-up of patients with hypertrophic cardiomyopathyin our setting.Methods: A retrospective cohort of patients with hypertrophic cardiomyopathy was studied, assessing functional class and clinicalevent occurrence from echocardiographic and cardiac magnetic resonance imaging studies.Results: A total of 259 patients with median follow-up of 3.5 years (2-10) were included in the study. Mean age was 56±16.8 yearsand 38.2% had obstructive forms of the disease. Sixty-seven percent of patients were in functional class I at follow-up onset. Duringthe follow-up period, overall mortality rate was 1.6% with 1.1% sudden death or appropriate defibrillator shock and 6.6% of patientsdeveloped atrial fibrillation. The rate of in-hospital admission for acute heart failure was 5.8% and 14.3% of patients had functionalclass worsening. A total of 22 alcohol septal ablation and 15 myectomy procedures were performed with significant symptom improvement.Conclusions: Follow-up of patients with hypertrophic cardiomyopathy showed low morbidity and mortality rate. The main adverseevent was functional class worsening, followed by the development of atrial fibrillation and heart failure, with a low rate of suddendeath.

Metadatos destacados

Colecciones
Argentine Journal of Cardiology

Editor

Sociedad Argentina de Cardiología

Fuente

Revista Argentina de Cardiología; Vol 84, No 3 (2016); 222-227, Argentine Journal of Cardiology; Vol 84, No 3 (2016); 222-227

Citación

Costabel, Juan Pablo et al., “Evolución a largo plazo de pacientes con miocardiopatía hipertrófica,” Archivo PPCT, consulta 2 de abril de 2026, http://archivoppct.caicyt.gov.ar/items/show/9192.

Dublin Core

Autor

Costabel, Juan Pablo
Ametrano, María C.
Vrancic, Mariano
Cura, Fernando
Talavera, María L.
Acosta, Adriana
Díez, Mirta
Sciancalepore, Agustina
Kuschnir, Paola
Avegliano, Gustavo

Fuente

Revista Argentina de Cardiología; Vol 84, No 3 (2016); 222-227
Argentine Journal of Cardiology; Vol 84, No 3 (2016); 222-227

Editor

Sociedad Argentina de Cardiología

Fecha

2016-06-28

Derechos

Los que firman al pié, certificamos que tenemos total responsabilidad por la conducción de este estudio y por el diseño y la interpretación de los datos. Nosotros escribimos el manuscrito y somos responsables por la decisión acerca del mismo. Cada uno de nosotros cumple la definición de autor como se afirma en el Comité Internacional de Editores de Revistas Médicas (International Committee of Medical Journal Editors, ver www.icmje.org). Nosotros hemos visto y aprobado el manuscrito final. Ni el artículo, ni ninguna parte esencial del mismo, incluido las tablas y las figuras, será publicado o admitido para arbitrar a otra parte antes de aparecer en la Revista.También notificamos haber leído la sección “conflicto de intereses”, y revelaríamos cualquiera que existiera. Dejamos constancia que si nuestro artículo se publicara en la RAC, cederíamos los derechos (copyright) a la Revista.Los documentos publicados en esta revista están bajo la licencia Creative Commons Atribución-NoComercial-Compartir-Igual 2.5 Argentina.
Those signing below certify that we have full responsibility for the conduction of this study and for the design and interpretation of the information. We wrote the manuscript and are responsible for its decision. Each of us fulfills the definition of authorship as stated by the International Committee of Medical Journal Editors ( www.icmje.org). We have signed and approved the final manuscript. Neither the manuscript, nor any essential part thereof, including tables and figures, will be published or accepted for refereeing elsewhere before being published in the Journal. We have also read the "Conflict of Interest" section and would disclose any existing. We state that if our manuscript is published in the RAC, we shall transfer the copyright to the Journal.

Idioma

eng
spa

Tipo

info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion