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Análisis retrospectivo de una población de pacientes con síndrome de Brugada y cardiodesfibrilador automático implantable;
Retrospective Analysis of Patients with Brugada Syndrome and Implantable Cardioverter Defibrillator

Creators:Abud, Atilio Marcelo; Servicio de Cardiología. Sanatorio San Geronimo.
Servicio de Cardiología Hospital José Maria Cullen, Carlessi, Adrián, Goyeneche, Raúl, Strada, Bruno, Arceluz, Martín, Fernández, Agutín, Vicario, Santiago, Amín, Ainelen, Becker, Carlos

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Descripción

Introducción El síndrome de Brugada es una anomalía eléctrica hereditaria con riesgo incrementado de muerte súbita. El cardiodesfibrilador automático implantable es el único tratamiento efectivo para la prevención de la muerte súbita, mientras que la conducta terapéutica en los pacientes  asintomáticos continúa siendo controversial Objetivo Evaluar la incidencia y causas de choques apropiados e inapropiados y las complicaciones relacionadas con el dispositivo. Identificar la relación de variables clínicas y del estudio electrofisiológico con la ocurrencia de choques apropiados. Material y Métodos Registro unicéntrico, retrospectivo de pacientes con síndrome de Brugada, con patrón electrocardiográfico tipo 1 espontáneo o inducido con infusión de ajmalina, a quienes se les implantó un cardiodesfibrilador automático implantable. Resultados Se incluyeron 21 pacientes, 18 hombres, edad media de 40 años. El dispositivo fue indicado por síntomas: respiración agónica nocturna, sincope y paro cardíaco resucitado o por un estudio electrofisiológico positivo en pacientes asintomáticos. En un seguimiento de 88 meses no hubo muertes, la tasa anual de choques apropiados fue del 1.9%, inferior a la de choques inapropiados (7.5%). Diez pacientes tuvieron complicaciones incluyendo infección del dispositivo y disturbios psiquiátricos La única variable relacionada significativamente con la presencia de choques apropiados fue la historia de fibrilación y fluter auricular. Conclusión Se observó una baja tasa anual de choques apropiados. Las dificultades en la estratificación de riesgo, la alta incidencia de choques inapropiados y la alta frecuencia de complicaciones, hacen recomendable una cuidadosa selección  para el implante de estos dispositivos, hasta encontrar predictores mas confiables de riesgo arrítmico.

Introduction: The Brugada syndrome is an inherited, electrical anomaly, with increased risk ofsudden cardiac death. Automatic cardioverter defibrillators are the only effective treatment to prevent sudden cardiac death, while therapy management in asymptomatic patients is still controversial.Objectives: The aims of the study were to evaluate the incidence and causes of appropriate and inappropriate shocks and the complications related to the device, and to identify the relationship of clinical and electrophysiological study variables with the incidence ofappropriate shocks.Methods: This was a single-center, retrospective registry of patients with type-1 electrocardiographic Brugada syndrome, either spontaneous or induced by ajmaline infusion, whowere recipients of automatic implantable cardioverter defibrillator.Results: Twenty-one patients were included in the study; 18 men, with average age of 40 years. The device was indicated due to the following symptoms: nocturnal agonalrespiration, syncope and resuscitated cardiac arrest, or positive electrophysiologicalstudy in asymptomatic patients. There were no deaths during follow-up of 88 months, and the annual rate of appropriate shocks was 1.9%, below that of inappropriate shocks (7.5%). Ten patients presented complications including device infection and psychiatric disorders. The only variable significantly related with the presence of appropriate shocks was history of fibrillation and atrial flutter.Conclusions: A low annual rate of appropriate shocks was observed. The difficulties in risk stratification, the high incidence of inappropriate shocks and the high frequency of complication sindicate need of careful patient selection for the implantation of thesedevices until more reliable predictors of arrhythmic risk are found.

Metadatos destacados

Colecciones
Argentine Journal of Cardiology

Editor

Sociedad Argentina de Cardiología

Fuente

Revista Argentina de Cardiología; Vol 82, No 1 (2014); 19-23, Argentine Journal of Cardiology; Vol 82, No 1 (2014); 19-23

Citación

Abud, Atilio Marcelo; Servicio de Cardiología. Sanatorio San Geronimo. Servicio de Cardiología Hospital José Maria Cullen et al., “Análisis retrospectivo de una población de pacientes con síndrome de Brugada y cardiodesfibrilador automático implantable,” Archivo PPCT, consulta 2 de abril de 2026, http://archivoppct.caicyt.gov.ar/items/show/8274.

Dublin Core

Autor

Abud, Atilio Marcelo; Servicio de Cardiología. Sanatorio San Geronimo.
Servicio de Cardiología Hospital José Maria Cullen
Carlessi, Adrián
Goyeneche, Raúl
Strada, Bruno
Arceluz, Martín
Fernández, Agutín
Vicario, Santiago
Amín, Ainelen
Becker, Carlos

Fuente

Revista Argentina de Cardiología; Vol 82, No 1 (2014); 19-23
Argentine Journal of Cardiology; Vol 82, No 1 (2014); 19-23

Editor

Sociedad Argentina de Cardiología

Fecha

2014-01-28

Derechos

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Those signing below certify that we have full responsibility for the conduction of this study and for the design and interpretation of the information. We wrote the manuscript and are responsible for its decision. Each of us fulfills the definition of authorship as stated by the International Committee of Medical Journal Editors ( www.icmje.org). We have signed and approved the final manuscript. Neither the manuscript, nor any essential part thereof, including tables and figures, will be published or accepted for refereeing elsewhere before being published in the Journal. We have also read the "Conflict of Interest" section and would disclose any existing. We state that if our manuscript is published in the RAC, we shall transfer the copyright to the Journal.

Idioma

spa
eng

Tipo

info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion