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RIΏ   endstream endobj startxref 116 %%EOF Ecografía Doppler strain 2D en la evaluación de la función ventricular en pacientes con diagnóstico reciente de hemocromatosis hereditaria - Archivo PPCT

Ecografía Doppler strain 2D en la evaluación de la función ventricular en pacientes con diagnóstico reciente de hemocromatosis hereditaria;
Two-dimensional Strain Echocardiography in the Evaluation of Ventricular Function in Patients with Newly Diagnosed Hereditary Hemochromatosis

Creators:Aladio, J. Martín, Yamasato, Florencia, Saad, Ariel K., Sordá, Juan, Grosso, Oscar, González Ballerga, Esteban, Daruich, Jorge, Berensztein, Sara

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Descripción

Introducción: La hemocromatosis hereditaria es una enfermedad genética que genera una sobrecarga sistémica de hierro, y en etapas avanzadas, puede afectar el corazón. El compromiso miocárdico precoz por esta enfermedad no ha sido suficientemente investigado.Objetivo: Comparar mediante ecocardiografía Doppler convencional y strain 2D un grupo de pacientes con diagnóstico recientede hemocromatosis hereditaria vs. un grupo control.Material y métodos: Se estudiaron pacientes con diagnóstico reciente de hemocromatosis hereditaria, no tratados. Se les realizó un ecocardiograma Doppler convencional y con strain bidimensional para evaluar la deformación longitudinal, radial y circunferencial, y el giro y torsión del ventrículo izquierdo.Resultados: Participaron 23 varones con hemocromatosis hereditaria (46 ± 18 años) y 20 sujetos control (45 ± 15 años). No hubo diferencias en los espesores y tamaños ventriculares. Los pacientes con hemocromatosis hereditaria tuvieron una fracciónde eyección del ventrículo izquierdo menor (59 ± 4% vs. 62 ± 4 %; p = 0,01). No hubo diferencias en cuanto a ESPAM, TAPSEu onda s´ del ventrículo izquierdo. Se observó una disminución significativa del strain en los pacientes con HH, con mayorc ompromiso de la deformación radial (37 ± 12 % vs. 55 ± 17 %; p = 0,01) y circunferencial (−19,5 ± 2,8 % vs. −22,5 ± 2,8 %;p = 0,001), y, en menor medida, de la longitudinal (−19 ± 1,8 % vs. −21,1 ± 2,5 %; p=0,04). También este grupo tuvo menor rotación apical, menor giro (17,7 ± 13° vs. 25 ± 7°; p = 0,03) y menor torsión (2,3 ± 1,8 °/cm vs. 3,3 ± 1,1 °/cm; p = 0,03). No hubo correlación entre los diferentes tipos de deformación y los parámetros bioquímicos del metabolismo férrico.Conclusiones: La ecocardiografía y especialmente la evaluación del strain 2D es capaz de detectar de manera temprana ligeras alteraciones de la mecánica ventricular en pacientes asintomáticos, con sobrecarga sistémica de hierro por hemocromatosis hereditaria.

Background: Hereditary hemochromatosis is a genetic disorder characterized by systemic iron overload which can involve theheart in advanced stages. Early myocardial involvement has not been thoroughly investigated.Objective: The aim of our study was to evaluate the performance of conventional Doppler-echocardiography and 2D strainechocardiography in a group of patients with newly diagnosed hereditary hemochromatosis vs. a control group.Methods: Patients with newly diagnosed hereditary hemochromatosis without treatment were included. All the patientsunderwent conventional Doppler echocardiography and 2D strain echocardiography with evaluation of left ventricular longitudinal,radial and circumferential strain, twist and torsion.Results: Twenty-three male patients with hereditary hemochromatosis (46±18 years) and 20 male controls (45±15 years)were included. There were no differences in ventricular dimensions and wall thickness. Left ventricular ejection fractionwas lower in patients with hereditary hemochromatosis (59±4% vs. 62±4%; p=0.01). There were no differences in MAPSE,TAPSE and left ventricular s’ velocity. There was a significant decrease in global strain in patients with hereditary hemochromatosis,with greater involvement of radial strain (37±12 % vs. 55±17%; p=0.01) and circumferential strain (-19.5±2.8% vs.-22.5±2.8%; p=0.001), and less involvement of longitudinal strain (-19±1.8% vs. -21.1±2.5%; p=0.04). Myocardial rotationshowed lower twist (17.7±13° vs. 25±7°; p=0.03) and lower torsion (2.3±1.8°/cm vs. 3.3±1.1 °/cm; p=0.03). There was nocorrelation between the different strain parameters and iron metabolism.Conclusions: Echocardiography, and particularly 2D strain analysis can detect early abnormalities of ventricular mechanicsin asymptomatic patients with systemic iron overload due to hereditary hemochromatosis.

Metadatos destacados

Colecciones
Argentine Journal of Cardiology

Editor

Sociedad Argentina de Cardiología

Fuente

Revista Argentina de Cardiología; Vol 87, No 6 (2019); 449-455, Argentine Journal of Cardiology; Vol 87, No 6 (2019); 449-455

Citación

Aladio, J. Martín et al., “Ecografía Doppler strain 2D en la evaluación de la función ventricular en pacientes con diagnóstico reciente de hemocromatosis hereditaria,” Archivo PPCT, consulta 2 de abril de 2026, http://archivoppct.caicyt.gov.ar/items/show/9641.

Dublin Core

Autor

Aladio, J. Martín
Yamasato, Florencia
Saad, Ariel K.
Sordá, Juan
Grosso, Oscar
González Ballerga, Esteban
Daruich, Jorge
Berensztein, Sara

Fuente

Revista Argentina de Cardiología; Vol 87, No 6 (2019); 449-455
Argentine Journal of Cardiology; Vol 87, No 6 (2019); 449-455

Editor

Sociedad Argentina de Cardiología

Fecha

2020-01-13

Derechos

Los que firman al pié, certificamos que tenemos total responsabilidad por la conducción de este estudio y por el diseño y la interpretación de los datos. Nosotros escribimos el manuscrito y somos responsables por la decisión acerca del mismo. Cada uno de nosotros cumple la definición de autor como se afirma en el Comité Internacional de Editores de Revistas Médicas (International Committee of Medical Journal Editors, ver www.icmje.org). Nosotros hemos visto y aprobado el manuscrito final. Ni el artículo, ni ninguna parte esencial del mismo, incluido las tablas y las figuras, será publicado o admitido para arbitrar a otra parte antes de aparecer en la Revista.También notificamos haber leído la sección “conflicto de intereses”, y revelaríamos cualquiera que existiera. Dejamos constancia que si nuestro artículo se publicara en la RAC, cederíamos los derechos (copyright) a la Revista.Los documentos publicados en esta revista están bajo la licencia Creative Commons Atribución-NoComercial-Compartir-Igual 2.5 Argentina.
Those signing below certify that we have full responsibility for the conduction of this study and for the design and interpretation of the information. We wrote the manuscript and are responsible for its decision. Each of us fulfills the definition of authorship as stated by the International Committee of Medical Journal Editors ( www.icmje.org). We have signed and approved the final manuscript. Neither the manuscript, nor any essential part thereof, including tables and figures, will be published or accepted for refereeing elsewhere before being published in the Journal. We have also read the "Conflict of Interest" section and would disclose any existing. We state that if our manuscript is published in the RAC, we shall transfer the copyright to the Journal.

Idioma

spa
eng

Tipo

info:eu-repo/semantics/article
info:eu-repo/semantics/publishedVersion